Familial primary pulmonary hypertension: when to get help
Go through these in order and stop at the first one that applies. If you are reading this for someone else, answer for them.
1
Is any of this happening now?
Call 911
Call emergency services for:
Severe breathlessness at rest
Fainting with slow recovery or injury
Severe or persistent chest pain
Blue or grey lips with marked breathing difficulty
Confusion, collapse, or inability to stay awake
A sudden interruption of continuous intravenous PAH medicine that cannot be restored immediately
Do not drive yourself for emergency care.
Other emergency signs, for anyone
Someone who is struggling to breathe, gasping, choking, or cannot get words out
Someone who has chest pain, tightness or pressure lasting more than a few minutes
Someone who has sudden weakness or drooping on one side of the face or body, slurred speech, or sudden confusion
Someone who is unconscious, or cannot be woken
Someone who is bleeding heavily and it will not stop with firm pressure
Someone who has had a seizure that will not stop, or does not wake up afterwards
Someone who has lips or skin that look pale, blue, grey or blotchy
Someone who you believe has taken an overdose or swallowed something poisonous
2
Is any of this happening?
Be seen today
Seek urgent medical advice for new fainting or near-fainting, new chest discomfort, rapidly increasing swelling, coughing up blood, or a sudden decline in exercise ability.
The article also says
Contact your pulmonary hypertension team if you have a gradual increase in breathlessness, tiredness, swelling, palpitations, or difficulty with activities that were previously manageable.
Report persistent medication side effects or problems using an infusion or inhaled treatment.
Every sign above is quoted from the sofidex article on Familial primary pulmonary hypertension. If you are not sure, err upward — it is always reasonable to be checked.